Juvenile nasopharyngeal angiofibromas (JNA) are a rare benign but locally aggressive vascular tumor. Epidemiology Juvenile nasopharyngeal angiofibromas. Introduction: Juvenile nasopharyngeal angiofibroma (NAJ) is a tumor with .. Acessos Cirúrgicos no Angiofibroma Nasofaríngeo Juvenil – Relato de caso e. Juvenile nasopharyngeal angiofibroma (JNA) is a rare and benign but locally aggressive fibrovascular tumor arising from the posterolateral wall of the.

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Juvenile nasopharyngeal angiofibroma | Radiology Reference Article |

A comparative study of surgical approches. A year-old male patient presented with a painless, progressive swelling in the upper jaw since 2 weeks. The genetic alterations observed more often involve sex chromosomes.

The infratemporal fossa approach for nasopharyngeal tumors. We analyzed findings in 20 patients who underwent angiofibrooma between and July – August Pages Biopsy should be avoided angiofjbroma to avoid extensive bleeding since the tumor is composed of blood vessels without a muscular coat.

JNA is an uncommon benign tumor predominantly affecting adolescent males.

Angiofibroma nasofaríngeo juvenil

The mean follow-up time was 85 months range, 10— months. Overlying mucosa appeared normal.

At the time of diagnosis, the mass classically involves the pterygopalatine fossa. Computed tomography CTmagnetic resonance imaging MRI and endoscopic examinations are the choice to define the extent and location of the tumor, allowing thus staged.

Other advantages include less surgical time, hospitalization, absence of visible scars, avoids complications such as epiphora, dysesthesia, trismus, and craniofacial deformities 2,5,14, Spontaneus regression of juvenile nasopharyngeal angiofibroma.

Unfortunately, this is difficult due to innocuous presenting symptoms. Juvenile nasopharyngeal angiofibroma JNA is a benign neoplasm of the nasopharynx. Current debate involves the hamartoma and vascular malformation theories. They account for only 0. Extensive bony destruction is usually not a feature, but rather bone is remodelled or resorbed. Professionals Review article English Clinical practice guidelines English Visual and neurological deficits may also appear when the orbit, skull base or endocranium are affected.


CT is particularly useful at delineating bony changes.

Am J Rhinol Allergy. These authors reported that tumour size and sinus extent of the disease are less important factors in predicting complete tumour excision, a philosophy which we share. Sarcoma Lymphoma Immature teratoma Melanoma. It presents as an innocuous, painless, unilateral nasal obstruction with or without epistaxis and rhinorrhea. This jjuvenil originates in the lateral wall of the nasal cavity, close to the superior border of the sphenopalatine foramen.

Check for errors and try again. Recently, due to the important role of endoscopic surgery in the treatment of these tumours, Snydermann et al. A typical staghorn type appearance is seen.

Endoscopic resection of JNA, alone or juvenkl combination with limited external approaches, is the treatment of choice for JNA in early stages; in certain centres with sufficient experience, JNA in advanced stages are also intervened.

Oronasal fistula a possible complication of juuvenil embolization in the management of juvenile nasopharyngeal angiofibroma. Symptoms of JNA depend on tumour location, size and extent.

If the involvement of the infratemporal fossa or the middle cerebral fossa is broad or intradural, it is safer to access through a lateral approach such as the subtemporal-preauricular approach.

Mesothelioma Malignant solitary fibrous tumor. Fisch classification, however, is currently accepted. Tumor recurrence in the long run has been a frustration.


Postoperative coronal C and axial D CT scan of the same patient, after tumour resection through endoscopic sinonasal surgery.

Endoscopic Surgery of Nasopharyngeal Angiofibroma

A concise classification system and appropriate treatment options. Bony erosion of the nasal cavity, hard palate and pterygoid plates is also common. With the latter approach, it is possible to expose and control the internal carotid artery and the temporal lobe. Tumors may invade the anterior fossa through the ethmoid and sphenoid sinuses, being more frequent in the middle fossa and remaining extradural 8,9, Diagnosis of JNA is made by complete history, clinical examination, radiography, nasal endoscopy and by using juvenol imaging techniques such as arteriography, computer tomography and magnetic resonance imaging.

Initially used to treat diseases such as non-neoplastic polyps and sinus disease, the development of the technique enabled the excision of benign and angiofobroma tumors located more recently 5.

On 4 occasions, more than one intervention by SNES had jvenil performed before referral to our centre. Extended osteoplastic maxillotomy for total excision of giant multicompartmental juvenile nasopharyngeal angiofibroma.

Although these masses are thought to arise from the region of the sphenopalatine foramenthey are usually sizeable at diagnosis, frequently with extension medially into the nasopharynxlaterally into the pterygopalatine fossa and over time beyond, into the orbitparanasal sinusesintracranial cavity and infratemporal fossa.

Case 7 Case angiofjbroma.

Eventually, the tumor may invade the infratemporal fossa and the middle cranial fossa.